Products

anti- GATM antibody

FNab03368 Catalogue No
Synonyms
AGAT
Host
Rabbit
Reactivity
Human, Mouse, Rat
Isotype
IgG
Application
ELISA, WB, IHC, IF
Product Information
Product Name
anti- GATM antibody
Catalogue No.
FNab03368
Size
100µg
Form
liquid
Purification
Immunogen affinity purified
Purity
≥95% as determined by SDS-PAGE
Host
Rabbit
Clonality
Polyclonal
Isotype
IgG
Storage
PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 24 months (Avoid repeated freeze / thaw cycles.)
Background
This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by mental retardation, language impairment, and behavioral disorders.
Immunogen Information
Immunogen
glycine amidinotransferase (L-arginine:glycine amidinotransferase)
Synonyms
AGAT
Observed MW
43 kDa
Application
Tested Application
ELISA, WB, IHC, IF
Recommended dilution
WB: 1:500 - 1:2000; IHC: 1:50 - 1:200; IF: 1:50 - 1:200
Uniprot information
Uniprot ID
P50440
Images
Immunohistochemistry of paraffin-embedded human liver using FNab03368 (GATM antibody) at dilution of 1:100
mouse kidney tissue were subjected to SDS PAGE followed by western blot with FNab03368 (GATM antibody) at dilution of 1:1000