FAH antibody

Synonyms:Beta diketonase antibody, FAA antibody, FAH antibody, Fumarylacetoacetase antibody, Fumarylacetoacetate hydrolase antibody
Catalogue No.:FNab02948Reactivity:Human, Mouse, Rat
Host:RabbitTested Application:ELISA, WB, IHC
Clonality:polyclonalIsotype:IgG
  • SPECIFICATIONS
Product Name
FAH antibody
Catalogue No.
FNab02948
Size
100μg
Form
liquid
Purification
Immunogen affinity purified
Purity
≥95% as determined by SDS-PAGE
Clonality
polyclonal
Isotype
IgG
Storage
PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.)
Immunogen
Immunogen
fumarylacetoacetate hydrolase (fumarylacetoacetase)
Alternative Names
Beta diketonase antibody, FAA antibody, FAH antibody, Fumarylacetoacetase antibody, Fumarylacetoacetate hydrolase antibody
UniProt ID
P16930
Observed MW
46 kDa
Application
Tested Applications
ELISA, WB, IHC
Recommended dilution
WB: 1:500 - 1:2000; IHC: 1:50 - 1:200
Validated Images
various lysates were subjected to SDS PAGE followed by western blot with FNab02948(FAH antibody) at dilution of 1:1000
Immunohistochemistry of paraffin-embedded human liver injury using FNab02948(FAH antibody) at dilution of 1:50
Background
This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT).