SGSH antibody

Synonyms:HSS antibody
Catalogue No.:FNab07813Reactivity:Human, Mouse, Rat
Host:RabbitTested Application:ELISA, WB, IHC
Clonality:polyclonalIsotype:IgG
  • SPECIFICATIONS
Product Name
SGSH antibody
Catalogue No.
FNab07813
Size
100μg
Form
liquid
Purification
Immunogen affinity purified
Purity
≥95% as determined by SDS-PAGE
Clonality
polyclonal
Isotype
IgG
Storage
PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.)
Immunogen
Immunogen
N-sulfoglucosamine sulfohydrolase
Alternative Names
HSS antibody
UniProt ID
P51688
Observed MW
57 kDa
Application
Tested Applications
ELISA, WB, IHC
Recommended dilution
WB: 1:500 - 1:2000; IHC: 1:50 - 1:100
Validated Images
HEK-293 cells were subjected to SDS PAGE followed by western blot with FNab07813( SGSH Antibody) at dilution of 1:1000
Immunohistochemistry of paraffin-embedded human stomach using FNab07813( SGSH Antibody) at dilution of 1:50
Background
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.